Surgical treatment of congenital bronchopulmonary disease in children

Abstract
From 1987 to 1992, 22 children (age 0 days-14 years) were operated forcongenital bronchopulmonary disease. One patient had a hamartoma. Fourchildren had a bronchogenic cyst, in 1 patient combined with an esophagealduplication. Intrapulmonary sequestration was diagnosed in 3 children; oneof whom had an esophageal duplication as well. Four children had localizedemphysema. In 1 patient histology showed rhabdomyosarcoma. A lobectomy wasperformed following chemotherapy but recurrence was not resectable at athird thoracotomy. Ten patients had cystic adenomatoid malformation, 6 weredependent on artificial ventilation before surgery. Three patients withcystic adenomatoid malformation died in hospital: 2 after pneumonectomy whowere shown to have bilateral disease and 1 died after bilobectomy and wasshown to have a hypoplastic contralateral lung. Hospital morbidity involved1 patient with recurrent pneumothorax, 2 with atelectasis of the operatedlung and 3 with prolonged artificial ventilation. Late mortality involved 1patient due to pulmonary rhabdomyosarcoma. After 1-26 months of follow-upthere were no late complications. Adequate multidisciplinary treatmentallows acceptable mortality and low morbidity in surgery for congenitalbronchopulmonary disease in children.

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