Primary pigmented micronodular disease of the adrenals

Abstract
Primary pigmented micronodular disease is a peculiar form of ACTH-indepen-dent Cushing’s syndrome characterized by the familial occurrence, the frequent association with malformations and the pathological adrenocortical picture consisting in micronod-ules with cellular deposition of lipofuscinic pigment. We describe here a case occurring in a 14-year-old girl.