Intrahepatic Biliary Tract Abnormalities in Children with Corrected Extrahepatic Biliary Atresia

Abstract
Three children with surgically corrected extrahepatic biliary atresia developed recurrent cholangitis associated with bile lakes that failed to drain via the hepatoportoenterostomy. Surgical or percutaneous drainage of these cysts was followed by resolution of the infection and spontaneous internal drainage. The ongoing inflammatory process may have resulted in intrahepatic biliary obstruction, which caused cholangitis and bile cysts. Successful treatment required not only antibiotics but drainage of bile lakes. Development of bile cysts is a new cause of recurrent cholangitis seen in extrahepatic biliary atresia.