Abstract
Summary: A description is given of a case of neonatal icterus and hemolytic anemia in a Danish boy in whose blood the activity of G‐6‐PD was markedly reduced. Icterus appeared already one hour after delivery and serum bilirubin reached a maximum value of 16.4 mg/100 ml on the fourth day of life. Anemia was present from the second day of life and progressed during the first month to a minimal concentration of Hb of 5.2 g/100 ml. Normal activities were found in his parents and sister.