Cystic Fibrosis Mutations Lead to Carboxyl-terminal Fragments That Highlight an Early Biogenesis Step of the Cystic Fibrosis Transmembrane Conductance Regulator

This publication has 45 references indexed in Scilit:

• Aggresomes: A Cellular Response to Misfolded Proteins
  The Journal of cell biology, 1998
• The Mechanism Underlying Cystic Fibrosis Transmembrane Conductance Regulator Transport from the Endoplasmic Reticulum to the Proteasome Includes Sec61β and a Cytosolic, Deglycosylated Intermediary
  Journal of Biological Chemistry, 1998
• UBIQUITIN AND THE CONTROL OF PROTEIN FATE IN THE SECRETORY AND ENDOCYTIC PATHWAYS
  Annual Review of Cell and Developmental Biology, 1998
• Regulated Co-translational Ubiquitination of Apolipoprotein B100
  Journal of Biological Chemistry, 1998
• Disease-Associated Mutations in Cytoplasmic Loops 1 and 2 of Cystic Fibrosis Transmembrane Conductance Regulator Impede Processing or Opening of the Channel
  Biochemistry, 1997
• Disease-associated Mutations in the Fourth Cytoplasmic Loop of Cystic Fibrosis Transmembrane Conductance Regulator Compromise Biosynthetic Processing and Chloride Channel Activity
  Published by Elsevier ,1996
• CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP
  Cell, 1995
• Multi-ion pore behaviour in the CFTR chloride channel
  Nature, 1993
• Molecular basis of defective anion transport in L cells expressing recombinant forms of CFTR
  Human Molecular Genetics, 1993
• Site-directed mutagenesis by overlap extension using the polymerase chain reaction
  Gene, 1989