The Dental Manifestations of the Morquio Syndrome (Mucopolysaccharidosis Type IV)
- 1 December 1975
- journal article
- research article
- Published by American Medical Association (AMA) in American Journal of Diseases of Children
- Vol. 129 (12) , 1445-1448
- https://doi.org/10.1001/archpedi.1975.02120490055017
Abstract
• This study describes in detail the enamel defects in a patient in whom the diagnosis of Morquio syndrome (muchopolysaccharidosis IV) has been supported both biochemically and roentgenographically. These defects are an apparently constant feature of the Morquio syndrome, and are therefore important aids to its differential diagnosis. The defects consist of abnormally thin enamel that is rough because of the numerous minute pits on its surface. The thinness of the enamel results in altered shape and discoloration of the teeth and in their being spaced. Apart from these defects, the enamel is histologically normal and is of normal hardness and radiodensity. (Am J Dis Child 129:1445-1448, 1975)Keywords
This publication has 3 references indexed in Scilit:
- Morquio-Brailsford disease A report of four affected sisters with absence of excessive keratan sulphate in the urineThe British Journal of Radiology, 1973
- Hereditary Disturbances of Enamel Formation and Calcification**From the Research Department, Loyola University, School of Dentistry, Chicago College of Dental Surgery, and the Department of Health and Welfare, Bureau of Health, Division of Dental Health, Augusta, Maine.The Journal of the American Dental Association, 1945
- Chondro-Osteo-Dystrophy. Roentgenographic and Clinical Features of a Child with Dislocation of VertebræThe British Journal of Radiology, 1931