Progressive dystrophy of the external ocular muscles (ocular myopathy). By L. G. Kiloh and S. Nevin (From the Neurological Department, King's College Hospital.) Brain 1951: 74; 115–143.
Making the point that subsequent involvement of the ocular muscles rarely complicates the regional or generalized weakness with which progressive muscular dystrophy presents, and then only in cases of Landouzy-Dejerine myopathy (facioscapulohumeral dystrophy) or myotonic dystrophy, (Leslie) Kiloh (1917–1997) and (Sam) Nevin (1905–1979) have noted ‘a number of cases of myopathy … in which ocular involvement was the primary and predominant feature’. ‘In some … only the levators of the upper lids were affected, but in others a complete external ophthalmoplegia developed over many years. The question arises whether these cases constitute a clinical group justifying the title ocular myopathy or whether they are merely rare atypical forms of muscular dystrophy … the pathology of those cases described as chronic progressive external ophthalmoplegia [is] considered by most authors to result from degeneration of the oculomotor nuclei, although no clear pathological anatomy has been established …’. They describe five cases.