The development of pulmonary vascular obstructive disease after successful Mustard operation in early infancy.

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Abstract
Pulmonary vascular obstructive disease developed postoperatively in an infant with aortopulmonary transposition and intact ventricular septum who underwent a Mustard operation at 3 mo. of age. Preoperative catheterization had shown normal pulmonary artery pressures. After surgery (4 mo.), catheterization showed pulmonary artery systolic pressure above the systemic level and a tortuous, attenuated pulmonary vascular tree visualized angiographically. Early corrective surgery may not preclude the development of pulmonary vascular obstructive disease in patients with aortopulmonary transposition.