A unique multisystemic syndrome of unknown origin

Abstract
A unique multisystemic syndrome of polyneuropathy, anasarca, polycythemia, pigmentation, and endocrinopathy that occurred outside of Japan is reported, along with the results of postmortem examination. A review of the literature on this syndrome is presented, and the possible etiological considerations are discussed. (Arch Intern Med137:1719-1721, 1977)