PAPULAR MUCINOSIS (SCLEROMYXOEDEMA) COMPLICATING DIFFUSE SYSTEMIC SCLEROSIS: CLINICAL FEATURES AND ELECTRON MICROSCOPE OBSERVATIONS
- 1 November 1992
- journal article
- case report
- Published by Oxford University Press (OUP) in Rheumatology
- Vol. 31 (11) , 779-782
- https://doi.org/10.1093/rheumatology/31.11.779
Abstract
Papular mucinosis (scleromyxoedema) is an uncommon disorder characterized by generalized papular eruption and cuta neous induration, which may be associated with a variety of extracutaneous manifestations. Although scleroderma and papular mucinosis share many features, they are clinically and histologically distinct entities. We report here a patient with diffuse scleroderma who developed superimposed papular mucinosis. Degranulating mast cells were a prominent ultra- structural finding in the involved skin. The occurrence of scleroderma and papular mucinosis, two uncommon cutaneous indurative diseases, in the same patient has not been described previously.Keywords
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