EXOMPHALOS-MACROGLOSSIA-GIGANTISM (VISCEROMEGALY) SYNDROME

1 February 1972

journal article
Published by American Roentgen Ray Society in American Journal of Roentgenology

Vol. 114 (2) , 264-267
https://doi.org/10.2214/ajr.114.2.264

Abstract

The 4 most characteristic clinical abnormalities of the Beckwith-Wiedemann syndrome are omphalocele or umbilical hernia, macroglossia, gigantism, and renal enlargement.Early recognition of this entity is imperative because of the high incidence of neonatal and infant death caused by hypoglycemia, and because of the suggested increased risk of the development of malignant abdominal tumor during childhood.

Keywords

MACROGLOSSIA GIGANTISM
RENAL ENLARGEMENT
WIEDEMANN SYNDROME
UMBILICAL HERNIA
INCREASED RISK
SUGGESTED INCREASED
MALIGNANT ABDOMINAL
EARLY RECOGNITION

This publication has 0 references indexed in Scilit: