Ichthyosis bullosa of Siemens responds well to low-dosage oral retinoids
- 1 November 1991
- journal article
- case report
- Published by Oxford University Press (OUP) in British Journal of Dermatology
- Vol. 125 (5) , 469-471
- https://doi.org/10.1111/j.1365-2133.1991.tb14776.x
Abstract
Summary Two patients with ichthyosis bullosa of Siemens (IBS) and one patient with bullous ichthyosiform erythroderma of Brocq (BIE) were treated with etretinate. Two additional patients with IBS received acitretin. All the patients had a marked improvement when on retinoids and the maintenance dose required was for IBS 10–25 mg per day. The patient with BIE was on a maintenance dose of 40–60 mg per day.Keywords
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