Correlations between branched-chain amino acids and branched-chain α-keto acids in blood in maple syrup urine disease
- 1 September 1978
- journal article
- research article
- Published by Elsevier in Clinica Chimica Acta; International Journal of Clinical Chemistry
- Vol. 88 (2) , 283-291
- https://doi.org/10.1016/0009-8981(78)90433-3
Abstract
No abstract availableThis publication has 28 references indexed in Scilit:
- Quinoxalinol derivatives of aliphatic 2-oxocarboxylic acids. Infrared and mass spectra of theO-trimethylsilylated compoundsJournal of Mass Spectrometry, 1977
- Determination of urinary phenylpyruvic acid in phenylketonurics by enol-borate methodClinica Chimica Acta; International Journal of Clinical Chemistry, 1974
- Branched-chain alpha-keto acids isolated as oxime derivatives: Relationship to the corresponding hydroxy acids and amino acids in Maple Syrup Urine DiseaseMetabolism, 1974
- Quantitative analysis of branched-chain α-keto acids as their trimethylsilylated oximesClinica Chimica Acta; International Journal of Clinical Chemistry, 1973
- Determination of α-keto acids as silylated oximes in urine and serum by combined gas chromatography-mass spectrometryClinica Chimica Acta; International Journal of Clinical Chemistry, 1973
- Gas chromatography—mass spectrometry studies of hipuric acid derivatives : I. Evaluation of methods for quantiative determination of hippuric acid. A search for benzoylsarcosine excretion in normal urineJournal of Chromatography A, 1973
- Derivatives for the identification and quantitative determination of some keto and aldo-carboxylic acids by gas-liquid chromatographyThe Analyst, 1972
- The configuration of the alloisoleucine present in maple syrup urine disease plasmaBiochemical Medicine, 1970
- Pathogenesis of maple-syrup-urine disease: observations during dietary management and treatment of coma by peritoneal dialysisBiochemical Medicine, 1969
- Metabolism of the white blood cells in maple-syrup-urine diseaseBiochimica et Biophysica Acta, 1960