Diencephalic Syndrome of Infantile Emaciation: Analysis of Literature and Report of Further 3 Cases
Open Access
- 1 June 1972
- journal article
- research article
- Published by BMJ in Archives of Disease in Childhood
- Vol. 47 (253) , 338-343
- https://doi.org/10.1136/adc.47.253.338
Abstract
Three children with diencephalic tumours are described, and an analysis of 45 cases from the literature together with our own 3 is presented. Boys are affected more frequently than girls (1·8:1) and the onset is during the first 12 months of life in 92% of cases. The main clinical features are emaciation, overactivity, pleasant disposition, and above-average height. The natural course of the disease is variable. Treatment is by radiotherapy. Operative intervention, except to relieve intracranial hypertension, is not usually indicated.Keywords
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