Fulminating parapontine epidermoid carcinoma in a four-year-old boy

Abstract
An unique case of primary intracranial epidermoid carcinoma in a 4‐year‐old boy is described. Its parapontine localization and malignant features combined to produce a fulminating clinical course simulating an intra‐axial mass lesion. The probable origin of the carcinoma from a benign epidermoid cyst is discussed. A review of the world's literature establishes not only the rarity of cyst‐derived intracranial epidermoid carcinoma, but also its unprecedented occurrence in a child.

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