THE ROLE OF THIAMIN IN MAPLE SYRUP URINE DISEASE
- 1 March 1982
- journal article
- review article
- Published by Wiley in Annals of the New York Academy of Sciences
- Vol. 378 (1 Thiamin) , 404-421
- https://doi.org/10.1111/j.1749-6632.1982.tb31214.x
Abstract
No abstract availableThis publication has 18 references indexed in Scilit:
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- Thiamine increases the specific activity of human liver branched chain α-ketoacid dehydrogenaseNature, 1975
- Maple Syrup Urine Disease: Coenzyme function and prenatal monitoringMetabolism, 1974
- Enzyme activity in classical and variant forms of maple syrup urine diseasePublished by Elsevier ,1972
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- The metabolism of leucine in tissue culture of skin fibroblasts of maple-syrup-urine diseaseBiochimica et Biophysica Acta, 1963
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