Vascular Manifestations in Patients With Ehlers-Danlos Syndrome
- 1 April 1982
- journal article
- research article
- Published by American Medical Association (AMA) in Archives of Surgery
- Vol. 117 (4) , 495-498
- https://doi.org/10.1001/archsurg.1982.01380280075015
Abstract
• Ehlers-Danlos syndrome (EDS) is clinically and genetically a heterogenous disorder of connective tissue synthesis. Seven clinical types of this disease have been identified and the underlying biochemical defects defined in types IV through VII. Unfortunately, most patients with major vascular complications of EDS have few, if any, of the commonly recognized musculoskeletal and cutaneous abnormalities. Recognition of the correct diagnosis and the application of accepted vascular surgical techniques may improve the morbidity and mortality for these patients. (Arch Surg 1982;117:495-498)This publication has 6 references indexed in Scilit:
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- Balloon catheter tamponade of major vascular woundsThe American Journal of Surgery, 1971
- Surgical aspects of the Ehlers-Danlos syndrome a survey of 100 casesBritish Journal of Surgery, 1969
- Surgical significance of the Ehlers-Danlos syndromeThe American Journal of Surgery, 1967
- Functional and Ultrastructural Abnormalities of Platelets in Ehlers-Danlos SyndromeAnnals of Internal Medicine, 1965
- Ehlers‐Danlos syndrome associated with multiple intracranial aneurysmsNeurology, 1964