PERINEURIOMA (LOCALIZED HYPERTROPHIC NEUROPATHY)

  • 1 January 1984
    • journal article
    • research article
    • Vol. 108  (7) , 557-560
Abstract
Three patients with localized hypertrophic neuropathy (LHN) has a painless, slowly progressive mononeuropathy overy many years, resulting in severe focal neurologic deficit. Grossly, the affected nerves showed a fusiform enlargement. Histologically, there was loss of nerve fibers, disorganization of the fascicular pattern, and proliferation of elongated cells with whorl formation. These cells exhibited no immunoreactivity for S-100 protein, and ultrastructural features set them apart from Schwann''s cells. LHN is not a disorder caused by hyperplasia of Schwann''s cells but a benign peripheral nerve tumor of perineurial cell origin. Perineurial and Schwann''s cells may not derive from the same precursor element.