Structure of Two Glycoasparagines Isolated from the Urine of Patients with Aspartyiglycosylaminuria (AGU)1

Abstract
The structures of two glycoasparagines composed of one mole each of N-acetylneuraminic acid, galactose, N-acetylglucosamine, and asparagine were determined by periodate oxidation, enzymatic degradation, and methylation analysis. The structures were NANAα2→3Galβ1→4GlcNAcβ→Asn and NANAα2→6Galβ1→4GlcNAcβ→Asn, respectively.