Yellowish flecks in Leber's congenital amaurosis.
Open Access
- 1 October 1984
- journal article
- research article
- Published by BMJ in British Journal of Ophthalmology
- Vol. 68 (10) , 727-731
- https://doi.org/10.1136/bjo.68.10.727
Abstract
The fundus abnormalities of Leber's congenital amaurosis are extremely variable, from normal to salt-and-pepper changes to typical retinitis pigmentosa. A less commonly seen appearance is that of multiple, irregular shaped, yellowish white flecks deep in the midperipheral retina in a periarteriolar distribution. The nasal fundus as well as the posterior pole are spared. Such a case is presented along with a four-year follow-up together with the fluorescein angiographic findings. The flecks appear to be specific for this entity.This publication has 22 references indexed in Scilit:
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