Characterization of the human ω‐oxidation pathway for ω‐hydroxy‐very‐long‐chain fatty acids
Open Access
- 8 January 2008
- journal article
- research article
- Published by Wiley in The FASEB Journal
- Vol. 22 (6) , 2064-2071
- https://doi.org/10.1096/fj.07-099150
Abstract
Very-long-chain fatty acids (VLCFAs) have long been known to be degraded exclusively in peroxisomes via β-oxidation. A defect in peroxisomal β-oxidation results in elevated levels of VLCFAs and is as...Keywords
Funding Information
- Association Européenne contre les Leucodystrophies
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