Multiple neuroepithelial (colloid) cysts

Abstract
A 4 yr old boy had 3 neuroepithelial cysts, 1 in the 3rd ventricle and 2 in the supratentorial subarachnoid space, and also had stenosis of the cerebral aqueduct, obstructive internal hydrocephalus, frontoethmoidal meningoencephalocele and right microphthalmia. The occurrence of these combined lesions supported the congenitally derived nature of the cysts. The cysts originated from neuroepithelium including ectopic ependyma-lined structures. The exception may be those cysts arising in or near the floor of the 3rd ventricle; these cysts could be derived from the cleft of Rathke''s pouch, an endodermal derivative. Folding of the neuroepithelium in contact with mesenchyma or neuroglial tissue was proposed as the mode of formation of most colloid cysts. Neuroepithelial cysts are apparently widely distributed throughout the CNS.