CONGENITAL SERUM PROTHROMBIN CONVERSION ACCELERATOR (SPCA) DEFICIENCY

Abstract
Coagulation studies performed on a 65-year-old white female with bleeding episodes from various sites since early childhood revealed the defect to be due to congenital serum prothrombin conversion accelerator (SPCA) deficiency. SPCA arises from a plasma precursor and is a relatively stable serum factor which, along with prothrombin, is adsorbed by BaSO4 and elutable by citrate. This is in contrast to plasma AC-globulin which is labile and not readily adsorbed by BaSO4.