Near-fatal Kearns-Sayre Syndrome

Abstract
The Kearns-Sayre syndrome is a relatively uncommon condition which occurs in childhood and is characterized by neurologic dysfunction and abnormalities in atrioventricular (AV) conduction. The high mortality rate is directly attrib utable to the cardiovascular manifestations of this syndrome. We report a case, with documentation of a "near-fatal" episode, and review the pertinent clinical features of the syndrome.