Asplenia syndrome with atypical cardiac anomalies
- 1 March 1982
- journal article
- case report
- Published by Springer Nature in Pediatric Cardiology
- Vol. 3 (1) , 35-38
- https://doi.org/10.1007/bf02082329
Abstract
Two infants with asplenia and complex cyanotic congenital heart disease showed unusual findings at cardiac catheterization. Each had a patent pulmonary outflow tract and a severe obstructive lesion of the aortic arch. These cases emphasize the heterogeneity of the asplenia-polysplenia syndromes. Pulmonary atresia or critical pulmonic stenosis is not an invariable accompaniment of the asplenia syndrome. Obstructive lesions of the aortic outflow tract, which occur in about 1/3 of patients with the polysplenia syndrome, also can occur with asplenia.Keywords
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