Lathosterolosis, a Novel Multiple-Malformation/Mental Retardation Syndrome Due to Deficiency of 3β-Hydroxysteroid-Δ5-Desaturase
- 1 October 2002
- journal article
- case report
- Published by Elsevier in American Journal of Human Genetics
- Vol. 71 (4) , 952-958
- https://doi.org/10.1086/342668
Abstract
No abstract availableKeywords
This publication has 30 references indexed in Scilit:
- Abnormal sterol metabolism in a patient with Antley‐Bixler syndrome and ambiguous genitaliaAmerican Journal of Medical Genetics, 2002
- Effects of sample storage on 7- and 8-dehydrocholesterol levels analysed on whole blood spots by gas chromatography–mass spectrometry-selected ion monitoringJournal of Chromatography B, 2002
- Mutations in the 3β-Hydroxysterol Δ24-Reductase Gene Cause Desmosterolosis, an Autosomal Recessive Disorder of Cholesterol BiosynthesisAmerican Journal of Human Genetics, 2001
- The Sonic Hedgehog–Patched–Gli Pathway in Human Development and DiseaseAmerican Journal of Human Genetics, 2000
- Role of Highly Conserved Residues in the Reaction Catalyzed by Recombinant Δ7-Sterol-C5(6)-Desaturase Studied by Site-Directed MutagenesisBiochemistry, 2000
- Smith-Lemli-Opitz Syndrome Is Caused by Mutations in the 7-Dehydrocholesterol Reductase GeneAmerican Journal of Human Genetics, 1998
- Molecular cloning and mapping of a human cDNA (SC5DL) encoding a protein homologous to fungal sterol-C5-desaturaseCytogenetic and Genome Research, 1996
- Eight Histidine Residues Are Catalytically Essential in a Membrane-Associated Iron Enzyme, Stearoyl-CoA Desaturase, and Are Conserved in Alkane Hydroxylase and Xylene MonooxygenaseBiochemistry, 1994
- Defective cholesterol biosynthesis in Smith-Lemli-Opitz syndromeThe Lancet, 1993
- A simple method for displaying the hydropathic character of a proteinJournal of Molecular Biology, 1982