H-Y POSITIVE 46 XX TRUE HERMAPHRODITISM WITH INTRASCROTAL UTERUS

Abstract
A rare form of true hermaphroditism with hypergonadotropic hypogonadism, gynecomastia, presence of an intrascrotal uterus and 46 XX karyotype is reported. It is the 3rd published case in the literature since 1965. The presence of H-Y antigen and of testicular tissue in the absence of a Y chromosome is discussed.