The Interaction of Alpha-Thalassemia and Homozygous Sickle-Cell Disease
- 17 June 1982
- journal article
- research article
- Published by Massachusetts Medical Society in New England Journal of Medicine
- Vol. 306 (24) , 1441-1446
- https://doi.org/10.1056/nejm198206173062402
Abstract
Patients with homozygous sickle-cell disease may be homozygous for alpha-thalassemia 2 (α–/α–), may be heterozygous for alpha-thalassemia 2 (α–/αα), or may have a normal alpha-globin-gene complement (αα/αα). We compared the clinical and hematologic features of 44 patients who had sickle-cell disease and homozygous alpha-thalassemia 2 with those of controls with the two hematologic conditions.This publication has 30 references indexed in Scilit:
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