Hereditary Angioneurotic Edema (HANE): Lack of Close Linkage between HLA Haplotypes and C1 Esterase Inhibitor Deficiency

Abstract
The HL-A haplotypes were defined in a series including 11 patients with HANE, 5 symptom-free subjects with pathological laboratory findings characteristic of HANE and their 33 healthy kinsmen. The subjects belonged to 2 Finnish families representing the more common form of HANE which is recognized by the immunochemically observed decrease of the inhibitor (C1-1NH) blocking the esterase activity of the 1st complement component. No linkage between HANE and the HL-A system was found.