Joubert Syndrome: a Case Confirmed by Computerized Tomography

Abstract
A new case of Joubert syndrome (agenesis of the cerebellar vermis, mental retardation, disturbance of respiratory rhythm, ataxia and abnormal eye-movements) is reported and the literature on 9 other cases is reviewed. The diagnosis was confirmed by computerized tomography. Early recognition of this syndrome is important for prognosis and genetic counseling.