RENAL-TRANSPLANTATION IN ALPORTS-SYNDROME - ANTI-GLOMERULAR BASEMENT-MEMBRANE GLOMERULONEPHRITIS IN THE ALLOGRAFT

  • 1 January 1982
    • journal article
    • research article
    • Vol. 57  (1) , 35-43
Abstract
Eleven patients with Alport''s syndrome had renal transplantation between 1963 and 1980. The mean follow-up is 6 yr (6 mo. to 14 yr). All 11 patients are currently alive. Ten have funcitoning grafts, and in 9 the serum creatinine concentration is < 2 mg/dl. Three patients received a 2nd allograft. Histologic study of the allografts that were lost revealed a diffuse crescentic glomerulonephritis with strongly positive linear IgG staining of the glomerular basement membrane in the allografts of 2 of the 3 patients; circulating antiglomerular basement membrane antibodies were present in 1 patient. These 2 patients had successful retransplantation and they remain well 1.5 and 4.5 yr later. Renal transplantation in patients with Alport''s syndrome is a worthwhile and very satisfactory procedure.